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01-06-2014 | Case Report

A case of congenital pyloric atresia with dystrophic epidermolysis bullosa

Authors: Scott S. Short, Christa N. Grant, Demetri Merianos, Dana Haydel, Henri R. Ford

Published in: Pediatric Surgery International | Issue 6/2014

Abstract

Pyloric atresia with epidermolysis bullosa (EB) dystrophica is a rare entity that may not be immediately recognized. We describe the fourth confirmed case of pyloric atresia associated with the dystrophic subtype of EB diagnosed by standard pathologic measures, and discuss the clinical disease features and recent advances in the pathophysiology.

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Title: A case of congenital pyloric atresia with dystrophic epidermolysis bullosa
Authors: Scott S. Short
Christa N. Grant
Demetri Merianos
Dana Haydel
Henri R. Ford
Publication date: 01-06-2014
Publisher: Springer Berlin Heidelberg
Published in: Pediatric Surgery International / Issue 6/2014
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-014-3505-y

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A case of congenital pyloric atresia with dystrophic epidermolysis bullosa

Abstract

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Abstract

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