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Intraosseous pseudotumor in a child with hypofibrinogenemia

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Abstract

Intraosseous pseudotumor (i.e. chronic, encapsulated, hemorrhagic fluid collection that can be seen in any portion of the tubular bones) is an uncommon complication of severe hemophilia; however, it can occur with other rare bleeding disorders. We present the case of an 11-year-old girl with hypofibrinogenemia who had multiple intramedullary lesions that were consistent with intramedullary pseudotumor associated with this rare bleeding disorder. Percutaneous biopsy of a pseudotumor is contraindicated due to the high prevalence of complications, including life-threatening bleeding. Therefore, radiologists should make the diagnosis with characteristic MR imaging findings in a patient with a severe coagulation disorder.

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Authors and Affiliations

  1. Department of Pediatric Radiology, Hacettepe University Medical School, Fakülteler Mah. Dirim sok 22/3, Cebeci, 06590, Ankara, Turkey

    H. Nursun Ozcan

  2. Department of Radiology, Hacettepe University Medical School, Ankara,, Turkey

    Fatma Bilge Ergen & Ustun Aydingoz

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  1. H. Nursun Ozcan
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  2. Fatma Bilge Ergen
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  3. Ustun Aydingoz
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Correspondence to H. Nursun Ozcan.

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Ozcan, H.N., Ergen, F.B. & Aydingoz, U. Intraosseous pseudotumor in a child with hypofibrinogenemia. Pediatr Radiol 44, 1458–1461 (2014). https://doi.org/10.1007/s00247-014-3004-2

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  • DOI: https://doi.org/10.1007/s00247-014-3004-2

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