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A Rare Report of Hypoplastic Coronary Arteries and Pulmonary Veins: A Case Report and Review of the Literature

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Abstract

Congenital coronary artery anomalies are estimated to affect about 1% of the general population. Hypoplastic coronary artery disease is an uncommon subset associated with significant mortality regardless whether another major cardiac anomaly is present. In this case report, we present an extremely rare case of an infant with hypoplastic coronary artery disease and hypoplastic pulmonary veins. A literature review pertinent to the clinical findings is also contained herein.

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Authors and Affiliations

  1. Division of Pediatric Cardiology, Department of Pediatrics, Rush University Medical Center, Chicago, IL, USA

    Raymond Morales, John Bokowski, Saif Aljemmali & Joshua Murphy

  2. Department of Pathology, Rush University Medical Center, Chicago, IL, USA

    Saroja Bharati

  3. Rosalind Franklin University of Sciences, North Chicago, IL, USA

    Saroja Bharati

  4. The Advocate Children’s Hospital, Oak Lawn, IL, USA

    Saroja Bharati

  5. Advocate Aurora Healthcare, Aurora, IL, USA

    Saroja Bharati

  6. Pediatric Cardiology, Department of Pediatrics, Northwestern University Feinberg School of Medicine, Chicago, IL, USA

    Ra-id Abdulla

Authors
  1. Raymond Morales
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  2. John Bokowski
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  3. Saif Aljemmali
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  4. Joshua Murphy
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  5. Saroja Bharati
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  6. Ra-id Abdulla
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Correspondence to Raymond Morales.

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Electronic supplementary material

Below is the link to the electronic supplementary material.

246_2020_2334_MOESM1_ESM.avi

ONLINE RESOURCE 1 Angiogram with selective injection into the right coronary artery demonstratingdiminutive collateral circulation. (AVI 14341 kb)

246_2020_2334_MOESM2_ESM.avi

ONLINE RESOURCE 2 Transthoracic echocardiogram parasternal short axis view demonstrating a patent rightcoronary artery with increased flow. (AVI 21603 kb)

246_2020_2334_MOESM3_ESM.avi

ONLINE RESOURCE 3 Transthoracic echocardiogram parasternal short axis view demonstrating a patent leftcoronary artery with early systolic flow reversal. (AVI 27903 kb)

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Morales, R., Bokowski, J., Aljemmali, S. et al. A Rare Report of Hypoplastic Coronary Arteries and Pulmonary Veins: A Case Report and Review of the Literature. Pediatr Cardiol 41, 1231–1237 (2020). https://doi.org/10.1007/s00246-020-02334-x

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  • DOI: https://doi.org/10.1007/s00246-020-02334-x

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