Summary
A 78-year-old man with amyloidosis involving the esophagus is described. The clinical and radiographic features resembled classic achalasia, while esophageal manometrics demonstrated aperistalsis, incomplete LES relaxation, but a normal LES resting pressure. A review of the literature suggests that esophageal amyloid may have variable presentations. This patient was successfully managed with forceful pneumatic bag dilatation.
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Costigan, D.J., Clouse, R.E. Achalasia-like esophagus from amyloidosis. Digest Dis Sci 28, 763–765 (1983). https://doi.org/10.1007/BF01312569
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DOI: https://doi.org/10.1007/BF01312569