Abstract
A syndrome of hyperostosis of the thoracic wall, nonspecific signs of inflammatory disease, and palmar and plantar pustulosis is described in eight patients (Table 1). Seven had intersternocostoclavicular ossification [12], and one had chromic recurrent multifocal osteomyelitis [2]. This complex of findings has been called “pustulotic arthro-osteitis” [5, 12]. This report emphasizes the periosseous soft tissue inflammation and the unexplained subclavian and mediastinal vein thrombosis seen in two patients [8]. Inflammatory periosseous and mediastinal lesions were seen on plain films in all eight patients and on computed tomographic (CT) scans in seven. Radiographs of the spine showed a spondyloarthropathy in three patients. This was characterized by ossification of the vertebral ligaments and sclerosis of the vertebral bodies. Awareness of the radiologic features of pustulotic arthro-osteitis is important because the clinical, biochemical and pathologic findings are often nonspecific and misleading [5, 8, 12].
Similar content being viewed by others
References
Beraneck L, Kaplan G, Benoist M, Bauchon JP, Prost A, Vassal JP, Kahn MF (1984) Hyperostose multiple avec scacro-iliite unilaterale. Une nouvelle spondylarthropathie. Presse Med 13:2001
Bjorksten B, Gustavson K, Eriksson B, Lindholm A, Nordstrom S (1978) Chronic recurrent multifocal osteomyelitis and pustulosis palmoplantaris. J Pediatr 93:227
Gerster JC, Lagier R, Nicod L (1985) Case report 311. Skeletal Radiol 14:53
Hoenel LC, Bradway WR, Constantini PJ (1980) Thrombophlebitis complicating sternocostoclavicular hyperostosis. Postgrad Med 68:113
Huaux JP, Maldague B, Malghem J, Meunier H, Noel H, Nagant-de-deux Chaisnes C (1986) Pustulotic arthroosteitis and related disorders in children and adults. (A report of seven cases.) J Belge Radiol 69:345
Jirik FR, Stein HB, Chalmers A (1982) Clavicular hyperostosis with enthesopathy, hypergammaglobulinemia, and thoracic outlet syndrome. Ann Intern Med 97:48
Keipert JA, Campbell PE (1970) Recurrent hyperostosis of the clavicles: an undiagnosed syndrome. Aust Paediatr J 6:97
Kohler H, Uehlinger E, Kutzner J, West TB (1977) Sternocostoclavicular hyperostosis: painful swelling of the sternum, clavicle, and upper ribs. Ann Intern Med 87:192
Resnick D (1980) Sternocostoclavicular hyperostosis. AJR 135:1278
Resnick D, Vint V, Poteshman NL (1981) Sternocostoclavicular hyperostosis. J Bone Joint Surg [Am] 63:1329
Sartoris JD, Schreiman JS, Kerr R, Resnik CS (1986) Sternocostoclavicular hyperostosis: a review and report of 11 cases. Radiology 158:125
Sonozaki H, Mitsui H, Miyanaga Y, Okitsu K, Igaraski M, Hayashi Y, Matsuura M, Azuma A, Okai K, Kawashima M (1981) Clinical features of 53 cases with pustulotic arthro-osteitis. Ann Rheum Dis 40:547
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
van Holsbeeck, M., Martel, W., Dequeker, J. et al. Soft tissue involvement, mediastinal pseudotumor, and venous thrombosis in pustulotic arthro-osteitis. Skeletal Radiol 18, 1–8 (1989). https://doi.org/10.1007/BF00366761
Issue Date:
DOI: https://doi.org/10.1007/BF00366761