Abstract
Paget's disease of the anus is a rare perianal disorder. The condition is often associated with underlying invasive carcinoma. The prognosis is poor when rectal adenocarcinoma is present. Five own cases of perianal Paget's disease are presented. In two of our cases an underlying adenocarcinoma was found in the anorectum. Adenocarcinoma is sweat gland ducts was found in one case. One patient developed an adenocarcinoma in the anorectal junction four years after the Paget diagnose. In only one of our cases no underlying adenocarcinoma was found.
Résumé
La maladie de Paget de l'anus est une lésion péri-anale rare. Cet état est souvent associé avec un cancer invasif sous-jacent. Le pronostic est mauvais lorsqu'un cancer du rectum est présent. 5 cas personnels de maladie de Paget péri-anale sont présentés. Dans deux de ces cas un cancer sous-jacent a été trouvé dans l'ano-rectum. Un cancer des canaux glandulaires sudoripares existait chez un malade. Un patient a développé un adénocarcinome de la jonction ano-rectale 4 ans après le diagnostic de maladie de Paget. Chez un seul de nos cas seulement il n'existait pas d'adénocarcinome sous-jacent.
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Goldman, S., Ihre, T., Lagerstedt, U. et al. Perianal Paget's disease: report of five cases. Int J Colorect Dis 7, 167–169 (1992). https://doi.org/10.1007/BF00360360
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DOI: https://doi.org/10.1007/BF00360360