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Scintigraphic findings and follow up in Erdheim-Chester disease

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Abstract

Two cases of Erdheim-Chester disease are presented: a 26-year-old white male patient with lipoidgranulomatosis of numerous long and flat bones and infiltration of pericardium, pleura, liver, spleen, thyroid, skin, conjunctiva, gingiva, and false vocal cord; and a 54-year-old white male with involvement of bones, orbits, brain, pericardium, and retroperitoneum. The scintigraphic findings in this disease are described, and a comprehensive review of the 27 previously reported cases is given including an assessment of the value of scintigraphy for diagnosis and follow up of this rare disease.

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Authors and Affiliations

  1. Department of Nuclear Medicine, Warren G. Magnuson Clinical Center, USA

    Dirk Sandrock & Ronald D. Neumann

  2. Laboratory of Pathology, National Cancer Institute, USA

    Maria J. Merino

  3. Cardiology Branch, National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, Maryland, USA

    Beate H. B. Scheffknecht

Authors
  1. Dirk Sandrock
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  2. Maria J. Merino
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  3. Beate H. B. Scheffknecht
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  4. Ronald D. Neumann
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Additional information

This work was partly supported by a grant from the Fogarty International Center (D.S.) and from the Erwin Schrödinger Stiftung (B.S.)

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Sandrock, D., Merino, M.J., Scheffknecht, B.H.B. et al. Scintigraphic findings and follow up in Erdheim-Chester disease. Eur J Nucl Med 16, 55–60 (1990). https://doi.org/10.1007/BF01566013

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  • DOI: https://doi.org/10.1007/BF01566013

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