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Reducing bodies in distal myopathy with rimmed vacuole formation

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Abstract

A 42-year-old woman with distal myopathy with rimmed vacuoles had intracytoplasmic inclusion bodies similar to those described in reducing body myopathy. Since these inclusions were found in fibers with high acid phosphatase activity and occasional rimmed vacuoles, their formation appeared to correlate with active myofibrillar degeneration, but their origin remains unknown.

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Authors and Affiliations

  1. Department of Ultrastructural Research, National Institute of Neuroscience, National Center of Neurology and Psychiatry, 187, Kodaira, Tokyo, Japan

    Beatriz H. Kiyomoto, Nobuyuki Murakami & Ikuya Nonaka

  2. Kitasato University East Hospital, 228, Sagamihara, Kanagawa, Japan

    Beatriz H. Kiyomoto

  3. National Center Hospital for Nervous, Mental and Muscular Disease, National Center of Neurology and Psychiatry, 187, Kodaira, Tokyo, Japan

    Jun Kishibayashi & Nobuhiko Sunohara

Authors
  1. Beatriz H. Kiyomoto
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  2. Nobuyuki Murakami
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  3. Jun Kishibayashi
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  4. Nobuhiko Sunohara
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  5. Ikuya Nonaka
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Kiyomoto, B.H., Murakami, N., Kishibayashi, J. et al. Reducing bodies in distal myopathy with rimmed vacuole formation. Acta Neuropathol 89, 109–111 (1995). https://doi.org/10.1007/BF00294268

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  • DOI: https://doi.org/10.1007/BF00294268

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