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Craniosynostosis

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Neurosurgery

Part of the book series: European Manual of Medicine ((EUROMANUAL))

Abstract

Craniosynostosis is the premature fusion of cranial sutures leading to an abnormal skull shape. Abnormal skull shapes were described by Hippocrates and Galen. Virchow [126], however, was the first to relate the abnormal skull shape to the premature fusion of cranial sutures. The extent of morphological and functional problems varies with the amount of sutures affected and is most pronounced in syndromic cases. Single-suture craniosynostosis is generally considered a purely cosmetic problem. However, increasing attention has been drawn to the occurrence of functional problems in single-suture synostosis. Raised intracranial pressure (ICP) is reported in up to 33% of patients [123, 105, 122]. Cognitive dysfunction, particularly affecting speech and learning abilities, is found to various degrees in all types of single-suture synostosis (Table 7.2.4). Problems with self-esteem occur in up to 10% [9].

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Authors and Affiliations

  1. Department of Pediatric Neurosurgery, Sophia Children’s Hospital, Erasmus University Medical Centre Rotterdam, Dr. Molewaterplein 60, Rotterdam, Netherlands

    Marie Lise C. van Veelen-Vincent

  2. Department of Plastic and Reconstructive Surgery, Erasmus University Medical Centre Rotterdam, Rotterdam, Netherlands

    Irene Mathijssen

  3. Craniofacial Unit, Department of Paediatric Neurosurgery, Hôpital Necker – Enfants Malades, Paris, René Descartes University, Paris, France

    Eric Arnaud

  4. Department of Paediatric Neurosurgery, Hôpital Necker – Enfants Malades, Paris, René Descartes University, Paris, France

    Dominique Renier & Federico Di Rocco

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  1. Marie Lise C. van Veelen-Vincent
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  2. Irene Mathijssen
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  3. Eric Arnaud
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  4. Dominique Renier
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  5. Federico Di Rocco
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Editors and Affiliations

  1. Department of Neurosurgery, Bogenhausen Academic Teaching Hospital, Technical University of Munich, Englschalkinger Straße 77, 81925, München, Germany

    Christianto B. Lumenta

  2. Istituto di Neurochirurgica, Università Cattolica del Sacro Cuore Policlinico Gemelli, Largo Gemelli 8, 00168, Rome, Italy

    Concezio Di Rocco

  3. Institute of Health Science and Technology, Faculties of Engineering, Science and Medicine, Aalborg University, Fredrik Bajers vej 7 D3, 9220, Aalborg East, Denmark

    Jens Haase

  4. Department of Neurosurgery, University of Groningen Medical Centre UMCG, 30.001, 9700 RB, Groningen, Netherlands

    Jan Jakob A. Mooij

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van Veelen-Vincent, M., Mathijssen, I., Arnaud, E., Renier, D., Di Rocco, F. (2010). Craniosynostosis. In: Lumenta, C., Di Rocco, C., Haase, J., Mooij, J. (eds) Neurosurgery. European Manual of Medicine. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-79565-0_29

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