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Juvenile Behçet’s Syndrome

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Behçet’s Syndrome

Abstract

Behçet’s syndrome (BS) may be seen in children; its frequency ranges between 2 and 5% among the BS population. It presents a somewhat different clinical picture than the adult form. Genders are equally affected. The mean age of onset is around 12 years. There may be prepubertal onset. While erythema nodosum is more prevalent among those with prepubertal onset, genital ulcers develop more frequently after puberty. Skin-mucosa lesions and vascular disease are less frequent while neurological disease is more common among juvenile patients compared to the adults. Despite its low frequency, large vessel disease is still severe and is the main associate of mortality. Similar to what is observed in adults, disease runs significantly more severe course among the boys.

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Authors and Affiliations

  1. Division of Rheumatology, Department of Medicine, Cerrahpasa Medical Faculty, University of Istanbul, Istanbul, Turkey

    Emire Seyahi

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  1. Emire Seyahi
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  2. Huri Özdoğan
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Correspondence to Emire Seyahi .

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Editors and Affiliations

  1. Hospital for Joint Diseases, Behçet's Syndrome Center, NYU Medical Center, East 20th Street 246, New York, 10003, New York, USA

    Yusuf Yazıcı

  2. , Department of Medicine, University of Istanbul, Istanbul, 34452, Turkey

    Hasan Yazıcı

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Seyahi, E., Özdoğan, H. (2010). Juvenile Behçet’s Syndrome. In: Yazıcı, Y., Yazıcı, H. (eds) Behçet’s Syndrome. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-5641-5_12

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  • DOI: https://doi.org/10.1007/978-1-4419-5641-5_12

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