Malnutrition is common in children with cystic fibrosis, and it contributes to both poor pulmonary and overall disease outcomes. But what are the challenges when trying to optimize nutrition?
Consensus recommendations from an international panel of experts on the use of lung ultrasound to optimize the management of neonatal respiratory distress.
Lung disease associated with refractory systemic juvenile idiopathic arthritis appears to be improved by allogeneic hematopoietic stem cell transplantation.
CPS are genetic disorders that significantly increase the risk of developing malignancies. The malignant features of CPS are well-studied, but recognizing their non-malignant features is crucial for early diagnosis in children and adolescents.
Growing numbers of young people are using e-cigarettes, despite warnings of respiratory effects and addiction. How can doctors tackle the epidemic, and what health effects should you prepare to manage in your clinics?
A 3-year-old with respiratory problems since birth was found to have multiple congenital anomalies affecting the airway including a posterior laryngeal cleft, a tracheal bronchus, and a very narrow distal trachea.
A rare case of new onset autoimmune adrenal insufficiency in a 7-year-old boy, presenting with severe cardiogenic shock requiring ECMO. Steroid replacement is critical.
This report of two brothers with plastic bronchitis underscores the role of influenza A virus infection and smoke inhalation as significant predisposing factors for the rare condition.
Cystic fibrosis (CF) is a rare genetic condition that impacts multiple organ systems, leading to chronic morbidity and significant care needs [ 1 ]. In 1978, the median survival of a child born with CF was 11 years [ 2 ]. Currently, the predicted …
Pulmonary complications are the leading cause of morbidity and mortality in pediatric patients with cystic fibrosis. Altered pharmacokinetic parameters in this population, as well as high inter- and intra-individual variability, complicate the …
Cystic fibrosis (CF) is a life-shortening multisystem disease resulting from mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, causing the most devastating phenotypes in the airway and pancreas. Significant advances …
For this review, a Medline search of English-language literature was performed. The European CF Society’s Standards of care, systematic reviews, guidelines regarding antibiotic treatment in CF and clinical trials considered relevant based on the …
Advances in patient-centered care and treatment for cardiopulmonary dysfunction are helping to increase life expectancy in DMD. This program equips multidisciplinary teams, including pediatric neurologists, pediatricians, pulmonologists, cardiologists, and endocrinologists, with key knowledge and skills to enhance care throughout the patient journey.
The escalating challenges of antibiotic resistance in bacterial pathogens have necessitated the exploration of alternative therapeutic strategies. Among these, bacteriophage therapy has regained attention as a promising approach to combat …
Cystic fibrosis (CF) is an inherited condition that leads to multiorgan dysfunction, especially in the respiratory, gastrointestinal, and reproductive tracts, with associated conditions including persistent pulmonary infection, liver disease …
In patients with cystic fibrosis (CF), chronically progressive lung damage is the major cause of morbidity and mortality [ 1 – 3 ]. Bronchial artery dilatation (BAD) is often diagnosed late at the time of pulmonary hemorrhage experienced by 9.1% of …
Respiratory syncytial virus (RSV) is a leading cause for global infant morbidity and mortality. The COVID-19 pandemic caused significant shifts in seasonality of RSV, and changes in disease severity have been matter of intense discussion. Between …
