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Published in: Journal of Medical Case Reports 1/2024

Open Access 01-12-2024 | Neck Pain | Case report

Neglected Sprengel’s deformity in an 80-year-old female cadaver: a case report

Authors: Shun Otsuka, Yuki Tamaki, Masaki Matsushita, Naoyuki Hatayama, Munekazu Naito

Published in: Journal of Medical Case Reports | Issue 1/2024

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Abstract

Background

Sprengel’s deformity is a congenital abnormality of the shoulder girdle. Because scapular retraction, such as the Green procedure, is usually performed during childhood to improve esthetics and shoulder function, Sprengel’s deformity is rarely found in older patients.

Case presentation

We presented a unique case of a Japanese female cadaver with Sprengel’s deformity at the age of 80 years. Anatomical dissection and radiological imaging revealed musculoskeletal anomalies associated with Sprengel’s deformity, including Klippel–Feil syndrome, presence of an omovertebral bone, and absence of the trapezius muscle. In addition, bilateral cervical ribs were in contact with the brachial plexus. These anomalies may lead to numbness, pain, and limited range of motion of the neck and upper girdle with aging.

Conclusions

Because most adult patients with Sprengel’s deformity experience neck pain and limited movement of the shoulder, the presented case is a rare case of neglected Sprengel’s deformity in an 80-year-old cadaver.
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Metadata
Title
Neglected Sprengel’s deformity in an 80-year-old female cadaver: a case report
Authors
Shun Otsuka
Yuki Tamaki
Masaki Matsushita
Naoyuki Hatayama
Munekazu Naito
Publication date
01-12-2024
Publisher
BioMed Central
Keyword
Neck Pain
Published in
Journal of Medical Case Reports / Issue 1/2024
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/s13256-024-04528-w

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