Myelolipoma is a benign tumour comprising both hematopoietic tissue and normal adipose tissue. It is a rare tumour found incidentally in adrenal glands on imaging, rarely reported in the extra-adrenal/perirenal region with less than 50 cases being reported in the literature. Even rarely, it presents bilaterally. We report a case of a 65-year-old male with bilateral extra-adrenal myelolipoma who underwent en bloc excision of bilateral tumours diagnosed preoperatively by radiological imaging. We reviewed the literature to look into the incidence, aetiology, imaging characteristics, diagnosis, treatment and follow-up in patients with extra-adrenal myelolipomas.
