Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis
DOI:
https://doi.org/10.1080/00015550152572985Abstract
A hereditary and an acquired type of C1-esterase inhibitor deficiency have been described. Manifestations characteristic of both forms include recurrent subcutaneous and submucosal angiooedema. Acquired C1-esterase inhibitor deficiency has been observed in association with lymphoproliferative disorders, malignancy, autoimmune diseases and infections. We report on a case with the acquired form of the disease accompanied by leucocytoclastic vasculitis. Treatment with antimalarial agents resulted in complete resolution of symptoms and signs. Furthermore, C1-esterase inhibitor concentration and activity, as well as C1 levels, all returned to normal.Downloads
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Published
2001-07-20
How to Cite
Farkas, H., Szongoth, M., Bély, M., Varga, L., Fekete, B., Karádi, I., & Füst, G. (2001). Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis. Acta Dermato-Venereologica, 81(4), 298–300. https://doi.org/10.1080/00015550152572985
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