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Isolated noncompaction of ventricular myocardium—detection during fetal life

Published online by Cambridge University Press:  19 August 2008

Thomas Kohl ,
Maria Villegas  and
Norman Silverman
Thomas Kohl
Affiliation:
From the University of California, San Francisco
Maria Villegas
Affiliation:
From the University of California, San Francisco
Norman Silverman*
Affiliation:
From the University of California, San Francisco
*
Dr. Norman H. Silverman, University of California, 505 Parnassus Avenue, Room M 342A/Box 0214, San Francisco, CA 94143, USA. Tel. (415) 476-5887; Fax. (415) 476-5875.
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Summary

Isolated noncompaction of ventricular myocardium is a rare cardiomyopathy with persistence of a myocardial architecture such as seen early in fetal development with numerous prominent trabeculations and deep intertrabecular spaces. Symptoms are related to cardiac failure, arterial embolism, and severe arrhythmias. Familial recurrence has been described. We describe a case where isolated noncompaction of ventricular myocardium could be recognized on an ultrasound study at 23 weeks gestation, thus supporting the developmental hypothesis.

Keywords

Noncompacrion of ventricular myocardiumcardiomyopathyfetal heart disease
Type
Brief Reports
Information
Cardiology in the Young , Volume 5 , Issue 2 , April 1995 , pp. 187 - 189
Copyright
Copyright © Cambridge University Press 1995

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References

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