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Current Pulmonology Reports
Published in:

12-08-2024 | Diagnostics in Respiratory Medicine | REVIEW

Cystic Lung Diseases: A Radiology Primer

Authors: Chenxi Wu, Carlos Sanchez, Kevin Oh, Michael Beal, Sanjeev Bhalla, Muhammad Naeem

Published in: Current Pulmonology Reports | Issue 3/2024

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Abstract

Purpose of Review

Cystic Lung Diseases (CLD) represent a diverse group of lung diseases characterized by the presence of intraparenchymal cysts. The purpose of this review is to provide an imaging primer and a proposed systematic approach to characterizing CLDs based on CT findings.

Recent Findings

Over the past decade, there have been tremendous advances in the understanding of pathophysiology and in therapeutic options for CLD. For example, Lymphangioleiomyomatosis (LAM) is now classified as low-grade metastasizing neoplasm and use of mTOR inhibitors (Sirolimus) has shown some promising results in the management. Providing an appropriate differential for CLD is pivotal for optimizing patient’s treatment.

Summary

Management of CLD is a multidisciplinary effort, with imaging playing a vital role. After initially excluding cyst-mimics, the differential diagnosis of CLD can be narrowed based on cyst features, distribution, and ancillary characteristics utilizing the systematic approach provided herein.
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Metadata
Title
Cystic Lung Diseases: A Radiology Primer
Authors
Chenxi Wu
Carlos Sanchez
Kevin Oh
Michael Beal
Sanjeev Bhalla
Muhammad Naeem
Publication date
12-08-2024

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