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Published in: Pediatric Cardiology 1/2024

07-11-2023 | Congenital Heart Anomaly | Case Report

Aorta Without Coronary Arteries: Anatomic Variants of a Rare Malformation

Authors: Julie Karila-Cohen, Daniela Laux, Lucile Houyel, Damien Bonnet

Published in: Pediatric Cardiology | Issue 1/2024

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Abstract

Absence of connection of both coronary arteries to the aorta is an extremely rare congenital malformation. Most cases reported are anatomic variants of anomalous left coronary artery to pulmonary artery, found in isolation or in association with other congenital heart defects. We describe here four cases of patients born without any coronary artery connected to the aorta, including two with an almost complete absence of epicardial coronary arteries, one with single coronary artery to the right pulmonary artery, and one with left ventricular connection of a single coronary artery. Those exceptional coronary malformations have a poor prognosis and are often diagnosed at autopsy. Total absence of epicardial coronary arteries, present in two of our patients and described only once in the literature, leads us to reconsider current knowledge of human coronary artery development.
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Metadata
Title
Aorta Without Coronary Arteries: Anatomic Variants of a Rare Malformation
Authors
Julie Karila-Cohen
Daniela Laux
Lucile Houyel
Damien Bonnet
Publication date
07-11-2023

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